產(chǎn)品編號 | bs-23057R-RBITC |
英文名稱 | Rabbit Anti-ACADS/RBITC Conjugated antibody |
中文名稱 | 羅丹明(RBITC)標(biāo)記的?;o酶A脫氫酶短鏈抗體 |
別 名 | ACAD3; Acyl Coenzyme A dehydrogenase, C2 to C3 short chain; Acyl-CoA dehydrogenase, C2 to C3 short chain; Acyl-CoA dehydrogenase, short chain; Acyl-Coenzyme A dehydrogenase, short chain; AI196007; Bcd-1; Bcd1; Butyryl CoA dehydrogenase; EC 1.3.99.2; SCAD; Short chain acyl CoA dehydrogenase; Short-chain specific acyl-CoA dehydrogenase, mitochondrial; Unsaturated acyl CoA reductase; ACADS_HUMAN. |
規(guī)格價(jià)格 | 100ul/2980元 購買 大包裝/詢價(jià) |
說 明 書 | 100ul |
研究領(lǐng)域 | 腫瘤 細(xì)胞生物 免疫學(xué) 轉(zhuǎn)錄調(diào)節(jié)因子 線粒體 |
抗體來源 | Rabbit |
克隆類型 | Polyclonal |
交叉反應(yīng) | (predicted: Human, Mouse, Rat, Pig, Cow, ) |
產(chǎn)品應(yīng)用 | ICC=1:50-200 IF=1:50-200
not yet tested in other applications. optimal dilutions/concentrations should be determined by the end user. |
分 子 量 | 45kDa |
性 狀 | Lyophilized or Liquid |
濃 度 | 1mg/ml |
免 疫 原 | KLH conjugated synthetic peptide derived from human ACADS |
亞 型 | IgG |
純化方法 | affinity purified by Protein A |
儲 存 液 | 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol. |
保存條件 | Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C. |
產(chǎn)品介紹 |
background: ACADS is a homotetramer mitochondrial flavoprotein, which is a member of the acyl CoA dehydrogenase family. This enzyme catalyzes the initial step of the mitochondrial fatty acid beta oxidation pathway. Mutations in this gene have been associated with Short Chain Acyl CoA Dehydrogenase Deficiency. Subcellular Location: Mitochondrion matrix. DISEASE: Defects in ACADS are the cause of acyl-CoA dehydrogenase short-chain deficiency (ACADSD) [MIM:201470]. It is an autosomal recessive disorder resulting in acute acidosis and muscle weakness in infants, and a form of lipid-storage myopathy in adults. Similarity: Belongs to the acyl-CoA dehydrogenase family. Database links: Entrez Gene: 35 Human Entrez Gene: 11409 Mouse Omim: 606885 Human SwissProt: P16219 Human SwissProt: Q07417 Mouse Unigene: 507076 Human Unigene: 18759 Mouse Unigene: 1167 Rat Important Note: This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications. |
| 在线观看无码视频 | 黄色视频网站免费在线观看 | 国产喷白浆一区二区三区动漫 | 久久久久久久久久久性爱 | 国产A级毛片久久久久久 | 日批视频在线免费观看 | 卡通欧美另类小说在线观看 | 国产精品嫩草AV城中村 | 91精品无码人妻系列 | 亚洲AV无码乱码精品国产白浆 | 精品裸体BBB书BBBBBB | 麻豆传媒国产特级无码毛片 | 水蜜桃AV无码专区亚洲AV麻豆 | 日本大片免aaa费观看视频 | 人一禽一性一交乱一区 | 少妇搡BBBB搡BBB搡视频一级 | 成人粉嫩蜜桃AV小网站 | 国产清纯大学生白嫩动态图 | 色欲av无码一区二区人妻 | 国产人妻一区二区三区久 | 美女高潮喷水网站一区二区三区 | 可以看国产黄色视频的网站 | 日本无码AⅤ波多野结衣巨 一本大道无码人妻精品专区 | 成人网站在线观看一区高清 | 午夜av色欲aV | 国产精品无码一级特黄 | 国产一级一片免费播放放a 国产精品嫩草AV城中村 | 男女啪啪啪抽搐动态图 | 97精品人妻一区二区三区 | 国产老熟女伦老熟妇露脸 | 蜜臀久久99精品久久久久久白杨根 | www.亚洲一区 | 无码人精品一区二区三区99v | 18岁无码国内精品综合88 | 国产欧美日韩综合精品一区二区 | 91人人妻人人澡人人爽人人精品99 | 久久久精品国产人妻喷水 | 人妻毛片A一级毛片免费看 亚州精品一区二区三区黄久 | 久久成人电影免费在线观看 | 美女视频黄a视频全免费网站樱花 |