强伦轩一级A片在线观看,中文字幕乱码人妻二区三区,鲁鲁狠狠狠7777一区二区,西西4444www无码精品
掃碼關注公眾號           掃碼咨詢技術支持           掃碼咨詢技術服務
  
客服熱線:400-901-9800  客服QQ:4009019800  技術答疑  技術支持  質量反饋  關于我們  聯(lián)系我們
少妇把腿扒开让我添69式mv,欧美丰满美乳XXⅩ高潮www
首頁 > 產(chǎn)品中心 > 標記一抗 > 產(chǎn)品信息
Rabbit Anti-NBEAL2/BF594 Conjugated antibody (bs-19031R-BF594)
訂購熱線:400-901-9800
訂購郵箱:sales@bioss.com.cn
訂購QQ:  400-901-9800
技術支持:techsupport@bioss.com.cn
說 明 書: 100ul  
100ul/2980.00元
大包裝/詢價
產(chǎn)品編號 bs-19031R-BF594
英文名稱 Rabbit Anti-NBEAL2/BF594 Conjugated antibody
中文名稱 BF594標記的蛋白激酶錨定蛋白樣蛋白2抗體
別    名 BDPLT4; GPS; NBEAL2; NBEL2_HUMAN; Neurobeachin-like protein 2; UNQ253/PRO290.  
規(guī)格價格 100ul/2980元 購買        大包裝/詢價
說 明 書 100ul  
研究領域 細胞生物  發(fā)育生物學  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應
產(chǎn)品應用 ICC=1:50-200 IF=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 303kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human NBEAL2
亞    型 IgG
純化方法 affinity purified by Protein A
儲 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產(chǎn)品介紹 background:
The protein encoded by this gene contains a beige and Chediak-Higashi (BEACH) domain and multiple WD40 domains, and may play a role in megakaryocyte alpha-granule biogenesis. Mutations in this gene are a cause of gray platelet syndrome. [provided by RefSeq, Dec 2011]

Function:
Probably involved in thrombopoiesis. Plays a role in the development or secretion of alpha-granules, that contain several growth factors important for platelet biogenesis.

Subcellular Location:
Endoplasmic reticulum.

Tissue Specificity:
Expressed in megakaryocytes.

DISEASE:
Gray platelet syndrome (GPS) [MIM:139090]: A rare platelet disorder characterized by a selective deficiency in the number and contents of platelet alpha-granules. It is associated with mild to moderate bleeding tendency and moderate thrombocytopenia. The platelets are enlarged and have a gray appearance on light microscopy of Wright-stained peripheral blood smears due to decreased granules.

Similarity:
Belongs to the WD repeat neurobeachin family.
Contains 1 BEACH domain.
Contains 5 WD repeats.

Database links:

Entrez Gene: 23218 Human

Omim: 614169 Human

SwissProt: Q6ZNJ1 Human

Unigene: 437043 Human



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權所有 2004-2026 m.nmgps.com 北京博奧森生物技術有限公司
通過國際質量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號: 00124Q34771R2M/1100
通過國際醫(yī)療器械-質量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號: CQC24QY10047R0M/1100
京ICP備05066980號-1         京公網(wǎng)安備110107000727號
91夜色视频在线观看 | 日韩无码性爱视频 | DVD人人人澡人人人爽 | 久久99精品久久久久久 | 91亚洲精品乱码久久久久久蜜桃 | 囯产精品久久久久久久 | 亚洲第一页 在线 | 91午夜理伦私人影院 | 午夜精品久久久久久久 | 插bbav淫色Av| 91成人一区二区 | 欧美成人网站在线观看 | 红桃黄色商品在线观看 | 欧性猛交ⅩXXX乱大交 | av在线播放网站 | 寡妇免费A片一级无极看 | 亚洲AV无码乱码精品国产玉蒲团 | 蜜桃秘 AV一区二区三区 | 亚洲人偷拍偷窥XXXX | 午夜yy一区二区三区伦 | 亚洲日韩在线中文字幕 | 国产精品国产三级国产专区53 | 又硬又粗进去好爽A片看 | 亚洲AV无码乱码精品国产白浆 | 黄色视频在线观看免费观看99re | av网站在线播放 | 亚洲国精产品二二三三区 | 精品国产乱码久久久久久88AV | 安徽妇搡BBBB搡BBBB按摩小说 | 色婷婷综合久久久中文字幕 | 日本一本久道熟妇人妻无码 | 亚洲成人av一区二区在线播放 | 国产精品国产高清国产 | 7777色情网黄A片免费看蜜臀 | 精品久久久久久久久久 | 免费A片呻吟高清视频播放 性一交一乱一色一视频麻豆 | 亚洲精品成人久久久久久 | 77777少妇AAAAA片毛片 | 黑人性Xxxx在线播放 | 十八禁在线在线播放 | 99 国产丝袜在线播放竹菊 |